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"documento" => "simple-article" "crossmark" => 0 "subdocumento" => "cor" "cita" => "Rev Clin Esp. 2014;214:353-4" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:2 [ "total" => 1291 "formatos" => array:2 [ "HTML" => 528 "PDF" => 763 ] ] "es" => array:11 [ "idiomaDefecto" => true "cabecera" => "<span class="elsevierStyleTextfn">Correspondencia</span>" "titulo" => "Lupus eritematoso subagudo inducido por terbinafina en un paciente con lupus eritematoso sistémico" "tienePdf" => "es" "tieneTextoCompleto" => "es" "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "353" "paginaFinal" => "354" ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "Lupus erythematosus induced by terbinafine in a patient with systemic lupus erythematosus" ] ] "contieneTextoCompleto" => array:1 [ "es" => true ] "contienePdf" => array:1 [ "es" => true ] "resumenGrafico" => array:2 [ "original" => 0 "multimedia" => array:7 [ "identificador" => "fig0005" "etiqueta" => "Figura 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 749 "Ancho" => 1000 "Tamanyo" => 103868 ] ] "descripcion" => array:1 [ "es" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">Se observa en espalda múltiples placas eritemato-edematosas, algunas de morfología anular y superficie levemente descamativa.</p>" ] ] ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "M.J. Concha-Garzón, G. Solano-López, C. García-García, R. García-Vicuña, E. Daudén" "autores" => array:5 [ 0 => array:2 [ "nombre" => "M.J." "apellidos" => "Concha-Garzón" ] 1 => array:2 [ "nombre" => "G." "apellidos" => "Solano-López" ] 2 => array:2 [ "nombre" => "C." "apellidos" => "García-García" ] 3 => array:2 [ "nombre" => "R." "apellidos" => "García-Vicuña" ] 4 => array:2 [ "nombre" => "E." "apellidos" => "Daudén" ] ] ] ] ] "idiomaDefecto" => "es" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S001425651400201X?idApp=WRCEE" "url" => "/00142565/0000021400000006/v1_201407221202/S001425651400201X/v1_201407221202/es/main.assets" ] "itemAnterior" => array:18 [ "pii" => "S0014256514001386" "issn" => "00142565" "doi" => "10.1016/j.rce.2014.03.014" "estado" => "S300" "fechaPublicacion" => "2014-08-01" "aid" => "949" "copyright" => "Elsevier España, S.L." "documento" => "simple-article" "crossmark" => 0 "subdocumento" => "cor" "cita" => "Rev Clin Esp. 2014;214:351-2" "abierto" => array:3 [ "ES" => false "ES2" => false "LATM" => false ] "gratuito" => false "lecturas" => array:2 [ "total" => 3292 "formatos" => array:2 [ "HTML" => 1995 "PDF" => 1297 ] ] "es" => array:10 [ "idiomaDefecto" => true "cabecera" => "<span class="elsevierStyleTextfn">Correspondencia</span>" "titulo" => "Síndrome PFAPA del adulto" "tienePdf" => "es" "tieneTextoCompleto" => "es" "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "351" "paginaFinal" => "352" ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "PFAPA syndrome in adults" ] ] "contieneTextoCompleto" => array:1 [ "es" => true ] "contienePdf" => array:1 [ "es" => true ] "autores" => array:1 [ 0 => array:2 [ "autoresLista" => "N. Ortega, M. Berenguer, A. Garre, M. Molina" "autores" => array:4 [ 0 => array:2 [ "nombre" => "N." "apellidos" => "Ortega" ] 1 => array:2 [ "nombre" => "M." "apellidos" => "Berenguer" ] 2 => array:2 [ "nombre" => "A." "apellidos" => "Garre" ] 3 => array:2 [ "nombre" => "M." "apellidos" => "Molina" ] ] ] ] ] "idiomaDefecto" => "es" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0014256514001386?idApp=WRCEE" "url" => "/00142565/0000021400000006/v1_201407221202/S0014256514001386/v1_201407221202/es/main.assets" ] "es" => array:14 [ "idiomaDefecto" => true "cabecera" => "<span class="elsevierStyleTextfn">Correspondencia</span>" "titulo" => "Esferocitosis hereditaria complicada con úlceras de miembros inferiores en una paciente embarazada" "tieneTextoCompleto" => true "saludo" => "<span class="elsevierStyleItalic">Sr. Director:</span>" "paginas" => array:1 [ 0 => array:2 [ "paginaInicial" => "352" "paginaFinal" => "353" ] ] "autores" => array:1 [ 0 => array:4 [ "autoresLista" => "V. Zubiaurre, G. Laporte, L. Sosa" "autores" => array:3 [ 0 => array:4 [ "nombre" => "V." "apellidos" => "Zubiaurre" "email" => array:1 [ 0 => "valezubi2@gmail.com" ] "referencia" => array:1 [ 0 => array:2 [ "etiqueta" => "<span class="elsevierStyleSup">¿</span>" "identificador" => "cor0005" ] ] ] 1 => array:2 [ "nombre" => "G." "apellidos" => "Laporte" ] 2 => array:2 [ "nombre" => "L." "apellidos" => "Sosa" ] ] "afiliaciones" => array:1 [ 0 => array:2 [ "entidad" => "Departamento Clínico de Medicina, Clínica Médica B, Hospital de Clínicas, Universidad de la República, Montevideo, Uruguay" "identificador" => "aff0005" ] ] "correspondencia" => array:1 [ 0 => array:3 [ "identificador" => "cor0005" "etiqueta" => "⁎" "correspondencia" => "Autor para correspondencia." ] ] ] ] "titulosAlternativos" => array:1 [ "en" => array:1 [ "titulo" => "Hereditary spherocytosis complicated with lower limb ulcers in a pregnant patient" ] ] "resumenGrafico" => array:2 [ "original" => 0 "multimedia" => array:7 [ "identificador" => "fig0005" "etiqueta" => "Figura 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 2103 "Ancho" => 1650 "Tamanyo" => 522886 ] ] "descripcion" => array:1 [ "es" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">En las imágenes a y b se observan úlceras perimaleolares izquierda y derecha, respectivamente previo a la esplenectomía. En las imágenes c y d se observa la evolución de las lesiones ulceradas pasados 3 meses de la esplenectomía.</p>" ] ] ] "textoCompleto" => "<span class="elsevierStyleSections"><p id="par0005" class="elsevierStylePara elsevierViewall">La esferocitosis hereditaria (EH) es la anemia hemolítica más frecuente en caucásicos con una prevalencia estimada de 0,4-1:5000<a class="elsevierStyleCrossRef" href="#bib0005"><span class="elsevierStyleSup">1</span></a>. Se presenta característicamente con hemólisis extracorpuscular, esplenomegalia e ictericia. Menos frecuentemente asocia hipertensión pulmonar, priapismo, litiasis vesicular y úlceras en miembros inferiores (MMII)<a class="elsevierStyleCrossRefs" href="#bib0010"><span class="elsevierStyleSup">2,3</span></a>. Reportamos un caso de EH que se presentó durante la gestación con úlceras de MMII y anemia como principal manifestación. Se trata de una mujer de 19 años de edad con diagnóstico de EH al año de vida. Ingresó en la 37 semana de edad gestacional y presenta anemia severa, esplenomegalia y úlceras en MMII. Destaca en el examen físico marcada palidez cutaneomucosa, taquicardia de reposo y esplenomegalia grado <span class="elsevierStyleSmallCaps">III</span>. En MMII presenta 2 úlceras de 7<span class="elsevierStyleHsp" style=""></span>cm de diámetro mayor en maléolo externo derecho y maléolo interno izquierdo (<a class="elsevierStyleCrossRef" href="#fig0005">fig. 1</a> a y b). Del estudio analítico destaca hemoglobina (Hb) de 6,7<span class="elsevierStyleHsp" style=""></span>g/dl, reticulocitosis 20%, bilirrubina total 3,55<span class="elsevierStyleHsp" style=""></span>mg/dl y bilirrubina indirecta 2,68<span class="elsevierStyleHsp" style=""></span>mg/dl. Durante el ingreso requirió reiteradas transfusiones de glóbulos rojos con persistencia de la hemólisis. A las 38 semanas se interrumpió la gestación alumbrando un recién nacido sin complicaciones. Durante el puerperio mantuvo anemia con Hb de 5,1<span class="elsevierStyleHsp" style=""></span>g/dl, marcadores de hemólisis elevados y persistencia de las úlceras en miembros, por lo que se decidió realizar esplenectomía laparoscópica. Presentó una evolución satisfactoria con descenso de los parámetros de hemólisis, al cuarto día de la postesplenectomía presentaba Hb de 11,6<span class="elsevierStyleHsp" style=""></span>g/dl y bilirrubina total de 0,61<span class="elsevierStyleHsp" style=""></span>mg/dl. Las úlceras de MMII presentaron curación parcial en 3 meses y total en 5 meses (<a class="elsevierStyleCrossRef" href="#fig0005">fig. 1</a> c y d). Las úlceras de MMII son manifestación inhabitual de la EH con una frecuencia menor del<span class="elsevierStyleHsp" style=""></span>2% (2;3). Suelen presentare en adultos o adolescentes en la segunda década de la vida, a los que no se realizó esplenectomía<a class="elsevierStyleCrossRefs" href="#bib0015"><span class="elsevierStyleSup">3,4</span></a>. La patogenia es desconocida, parece jugar un papel fundamental la anoxia tisular secundaria a pobre oxigenación aportada por los esferocitos en zonas pobremente vascularizadas y expuestas a traumatismos (sector distal de MMII)<a class="elsevierStyleCrossRef" href="#bib0020"><span class="elsevierStyleSup">4</span></a>. Existen pocos casos descritos en la literatura<a class="elsevierStyleCrossRefs" href="#bib0025"><span class="elsevierStyleSup">5–7</span></a> y la casi totalidad evolucionaron a la curación tras esplenectomía. El rol curativo de la misma (que solo resuelve la hemólisis extravascular y deja intactos los esferocitos), pone en duda el mecanismo central anoxo-isquémico planteado en la patogenia de las úlceras. Durante la gestación, la mayor complicación de la EH es la anemia, usualmente más grave y capaz de determinar complicaciones fetales, que puede agravarse por la hemodilución propia de la gestación. Con respecto a los resultados obstétricos algunos autores han comunicado una mayor tasa de pérdida del embarazo, pero ello es controvertido<a class="elsevierStyleCrossRef" href="#bib0040"><span class="elsevierStyleSup">8</span></a>. Existe acuerdo en que los resultados maternos y fetales mejoran notoriamente en las pacientes esplenectomizadas<a class="elsevierStyleCrossRef" href="#bib0040"><span class="elsevierStyleSup">8</span></a>.</p><elsevierMultimedia ident="fig0005"></elsevierMultimedia></span>" "pdfFichero" => "main.pdf" "tienePdf" => true "multimedia" => array:1 [ 0 => array:7 [ "identificador" => "fig0005" "etiqueta" => "Figura 1" "tipo" => "MULTIMEDIAFIGURA" "mostrarFloat" => true "mostrarDisplay" => false "figura" => array:1 [ 0 => array:4 [ "imagen" => "gr1.jpeg" "Alto" => 2103 "Ancho" => 1650 "Tamanyo" => 522886 ] ] "descripcion" => array:1 [ "es" => "<p id="spar0005" class="elsevierStyleSimplePara elsevierViewall">En las imágenes a y b se observan úlceras perimaleolares izquierda y derecha, respectivamente previo a la esplenectomía. En las imágenes c y d se observa la evolución de las lesiones ulceradas pasados 3 meses de la esplenectomía.</p>" ] ] ] "bibliografia" => array:2 [ "titulo" => "Bibliografía" "seccion" => array:1 [ 0 => array:2 [ "identificador" => "bibs0005" "bibliografiaReferencia" => array:8 [ 0 => array:3 [ "identificador" => "bib0005" "etiqueta" => "1" "referencia" => array:1 [ 0 => array:2 [ "contribucion" => array:1 [ 0 => array:2 [ "titulo" => "Clinical and hematologic features of 300 patients affected by hereditary spherocytosis grouped according to the type of the membrane protein defect" "autores" => array:1 [ 0 => array:2 [ "etal" => true "autores" => array:6 [ 0 => "M. Mariani" 1 => "W. Barcellini" 2 => "C. Vercellati" 3 => "A.P. Marcello" 4 => "E. Fermo" 5 => "P. 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Szakacs" ] ] ] ] ] "host" => array:1 [ 0 => array:1 [ "Revista" => array:7 [ "tituloSerie" => "Arch Gynecol Obstet" "fecha" => "1993" "volumen" => "253" "paginaInicial" => "37" "paginaFinal" => "42" "link" => array:1 [ 0 => array:2 [ "url" => "https://www.ncbi.nlm.nih.gov/pubmed/8328819" "web" => "Medline" ] ] "itemHostRev" => array:3 [ "pii" => "S0022347611002460" "estado" => "S300" "issn" => "00223476" ] ] ] ] ] ] ] ] ] ] ] ] "idiomaDefecto" => "es" "url" => "/00142565/0000021400000006/v1_201407221202/S0014256514001234/v1_201407221202/es/main.assets" "Apartado" => array:4 [ "identificador" => "992" "tipo" => "SECCION" "es" => array:2 [ "titulo" => "Correspondencia" "idiomaDefecto" => true ] "idiomaDefecto" => "es" ] "PDF" => "https://static.elsevier.es/multimedia/00142565/0000021400000006/v1_201407221202/S0014256514001234/v1_201407221202/es/main.pdf?idApp=WRCEE&text.app=https://revclinesp.es/" "EPUB" => "https://multimedia.elsevier.es/PublicationsMultimediaV1/item/epub/S0014256514001234?idApp=WRCEE" ]
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2016 June | 0 | 16 | 16 |
2016 May | 0 | 10 | 10 |
2016 April | 0 | 14 | 14 |
2016 March | 0 | 14 | 14 |
2016 February | 0 | 9 | 9 |
2016 January | 0 | 1 | 1 |
2015 December | 0 | 1 | 1 |
2015 November | 0 | 5 | 5 |
2015 October | 0 | 1 | 1 |